Publications - PulmoTension

Retrouvez les publications scientifiques majeures relatives à l’hypertension pulmonaire auxquelles les membres des centres de référence et de compétence PulmoTension ont contribué.

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05/2026
The preponderance of genetic variations in paediatric pulmonary hypertension (nouvel onglet)

Grynblat J, Eyries M, Ambar-Akkaoui M, Levy M, Meot M, Szezepanski I, Ranchoup J, Callegari A, Karila-Cohen J, Bonnet C, Marijon P, Champ J, Coulet F, Ovaert C, Perros F, Antigny F, Maragnes P, Vaksmann G, Humbert M, Malekzadeh Milani SG, Montani D, Bonnet D

Respir Med Res. 2026 May;89:101277. doi: 10.1016/j.resmer.2026.101277. Epub 2026 Apr 21. PMID: 42114419
04/2026
Pulmonary hypertension associated with hereditary haemorrhagic telangiectasia: from genetics to clinical management (nouvel onglet)

Jutant EM, Grynblat J, Pyrrait M, Lechartier B, Olitsky S, Ghigna MR, Dupuis-Girod S, Coulet F, Savale L, Humbert M, Ataya A, Montani D

Eur Respir J. 2026 Apr 16;67(4):2502322. doi: 10.1183/13993003.02322-2025. PMID: 41713948.
02/2026
Management of pulmonary arterial hypertension in systemic sclerosis: from classical treatments to new horizons (nouvel onglet)

Villa A, Sanges S, Sobanski V, Lamblin N, Rosato E, Godinas L, Hachulla E, Delcroix M, Montani D, Launay D

Eur Respir Rev. 2026 Feb 18;35(179):250137. doi: 10.1183/16000617.0137-2025. PMID: 41708122; PMCID: PMC12914380.
02/2026
International Liver Transplantation Society practice guideline update on portopulmonary hypertension (nouvel onglet)

DuBrock HM, Savale L, Sitbon O, Raevens S, Kawut SM, Fallon MB, Heimbach JK, Chadha RM, Crespo G, Ramsay MAE, Krowka MJ

Liver Transpl. 2026 Feb 1;32(2):296-314. doi: 10.1097/LVT.0000000000000600. Epub 2025 Mar 18. PMID: 40094355; PMCID: PMC12799263
12/2025
Response to correspondence on ‘Pulmonary arterial hypertension in adults with Still’s disease: another pulmonary manifestation associated with HLA-DRB1*15’ by Boucly A, et al. (nouvel onglet)

Mitrovic S, Boucly A, Sitbon O, Fautrel B, Montani D

Ann Rheum Dis. 2025 Dec;84(12):e69-e70. doi: 10.1016/j.ard.2025.09.004. Epub 2025 Oct 1. PMID: 41038765
11/2025
Diuretic adherence in patients with pre-capillary pulmonary hypertension: insights from the PHARE study (nouvel onglet)

Le Bozec A, Cohen SD, Montani D, Boucly A, Guignabert C, Roche A, Al Kahf S, Beurnier A, Sitbon O, Jaïs X, Jevnikar M, Humbert M, Savale L, Chaumais MC

ERJ Open Res. 2025 Nov 17;11(6):00110-2025. doi: 10.1183/23120541.00110-2025. PMID: 41257177; PMCID: PMC12621130
11/2025
The activin pathway in chronic thromboembolic pulmonary hypertension: a potential biomarker for residual pulmonary hypertension after endarterectomy (nouvel onglet)

Cuomo A, Normand C, Thuillet R, Jaffrezic T, Tu L, Jaïs X, Jevnikar M, Montani D, Boucly A, Sitbon O, Mercurio V, Fadel E, Mercier O, Guignabert C, Humbert M, Savale L

ERJ Open Res. 2025 Nov 10;11(6):01302-2024. doi: 10.1183/23120541.01302-2024. PMID: 41220827; PMCID: PMC12598586
11/2025
Cardiopulmonary Hemodynamic Determinants of Long-Term Survival in Sickle Cell Disease: Insights from the ETENDARD Study (nouvel onglet)

Savale L, d'Humières T, Boucly A, Habibi A, Lionnet F, Loko G, Inamo J, De Luna G, Al Kahf S, Chantalat-Auger C, Maitre B, Jaïs X, Montani D, Sitbon O, Parent F, Simonneau G, Galacteros F, Audureau E, Bartolucci P, Humbert M

Am J Respir Crit Care Med. 2025 Nov;211(11):2096-2104. doi: 10.1164/rccm.202502-0353OC. PMID: 40938591; PMCID: PMC12618979
11/2025
Evolving paradigms in pulmonary hypertension: Highlights of the 6th French Pulmonary Hypertension Network Meeting (nouvel onglet)

Boucly A, Beauvais A, Lacoste-Palasset T, Jevnikar M, Riou M, Solinas S, Antigny F, Bauer F, Bertoletti L, Bonnet D, Chaouat A, Cottin V, D'Alto M, Delcroix M, Dewavrin MG, Guignabert C, Hascoet S, Kiely DG, Jaïs X, Jutant EM, Lamblin N, Mercier O, Moceri P, Noel-Savina E, Picard F, Trembath R, Tromeur C, Vachiery JL, Savale L, Humbert M, Sitbon O, Montani D; on behalf on the French PH Network

Respir Med Res. 2025 Nov;88:101215. doi: 10.1016/j.resmer.2025.101215. Epub 2025 Oct 9. PMID: 41172670
11/2025
Pulmonary arterial stiffness as the main correlate of effective arterial elastance in pre- and post-capillary pulmonary hypertension (nouvel onglet)

Chemla D, Beurnier A, Gerges C, Jaïs X, Boucly A, Savale L, Sitbon O, Humbert M, Montani D, Hervé P

Respir Med Res. 2025 Nov;88:101204. doi: 10.1016/j.resmer.2025.101204. Epub 2025 Sep 4. PMID: 41067037

Rechercher une publication :

The preponderance of genetic variations in paediatric pulmonary hypertension (nouvel onglet)

Pulmonary hypertension associated with hereditary haemorrhagic telangiectasia: from genetics to clinical management (nouvel onglet)

Management of pulmonary arterial hypertension in systemic sclerosis: from classical treatments to new horizons (nouvel onglet)

International Liver Transplantation Society practice guideline update on portopulmonary hypertension (nouvel onglet)

Response to correspondence on ‘Pulmonary arterial hypertension in adults with Still’s disease: another pulmonary manifestation associated with HLA-DRB1*15’ by Boucly A, et al. (nouvel onglet)

Diuretic adherence in patients with pre-capillary pulmonary hypertension: insights from the PHARE study (nouvel onglet)

The activin pathway in chronic thromboembolic pulmonary hypertension: a potential biomarker for residual pulmonary hypertension after endarterectomy (nouvel onglet)

Cardiopulmonary Hemodynamic Determinants of Long-Term Survival in Sickle Cell Disease: Insights from the ETENDARD Study (nouvel onglet)

Evolving paradigms in pulmonary hypertension: Highlights of the 6th French Pulmonary Hypertension Network Meeting (nouvel onglet)

Pulmonary arterial stiffness as the main correlate of effective arterial elastance in pre- and post-capillary pulmonary hypertension (nouvel onglet)